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The first case of a DSRCT was recorded in 1989, and about 200 cases have been diagnosed since then. The disease is most common in Caucasian boys. Although researchers think a problem with the genes may cause DSRCT, this has not been proven.
Since DSRCT often is not diagnosed until the cancer is advanced, tumors grow large and spread through the lymph system or blood stream to other parts of the body. They can spread to many areas of the body, including the lymph nodes, lungs, bone and liver. Other types of cancer, including rhabdomyosarcoma, may be in the abdomen as well.
DSRCT is a dangerous type of cancer that often is resistant to treatment and frequently comes back after treatment.
Learn more about desmoplastic small round cell tumors:
- Desmoplastic small round cell tumor symptoms
- Desmoplastic small round cell tumor diagnosis
- Desmoplastic small round cell tumor treatment
In rare cases, DSRCT may be passed down from one generation to the next. Genetic counseling may be right for you. Visit our genetic testing page to learn more.
Why choose MD Anderson for your desmoplastic small round cell tumor treatment?
A team of highly focused renowned physicians, including surgeons, oncologists and radiologists, as well as a specialized support staff of nurses, physician’s assistants and others follow your child from diagnosis through treatment.
DSRCT often is difficult to diagnose. The Children’s Cancer Hospital utilizes the most advanced technology and techniques to pinpoint the cancer. We are at the forefront of discovering new therapies to help manage DSRCT, including:
- HIPEC (hyperthermic peritoneal perfusion with chemotherapy) which was pioneered at Children’s Cancer hospital, combines surgery with heated chemotherapy for a safe and often effective treatment. It has been shown to extend survival time in many patients.
- Targeted therapies that help fight DSRCT at the cellular level
Treating the whole child
Children’s Cancer Hospital is designed just for children, with a full range of services and amenities that help make the child and family’s experience as comfortable as possible. We go beyond medical care to deliver a comprehensive experience that treats the whole child.
And, at Children’s Cancer Hospital, you’re surrounded by the strength of one of the nation’s top cancer centers.
MD Anderson is a big organization, but it’s welcoming and it makes you feel safe. Help was always available
MD Anderson patients have access to clinical trials offering promising new treatments that cannot be
found anywhere else.
Find the latest news and information about desmoplastic small round cell tumors in our Knowledge Center, including blog posts, articles, videos, news releases and more.
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Prevention & Screening
Many cancers can be prevented with lifestyle changes and regular screening.